Biliary atresia associated with hypoplastic left heart syndrome: A case report and review of the literature

Authors

Daniel J. Becker, University of Michigan Health System, United States
Saleem Islam, University of Michigan Health System, United StatesFollow
James D. Geiger, University of Michigan Health System, United States

Document Type

Case Report

Department

Paediatric Surgery

Abstract

Biliary atresia is a cholestatic disorder of infancy that is associated with other anatomic anomalies in approximately 20% of cases. These frequently are defects in situs determination and laterality, causing syndromes of heterotaxy and complex heart defects. The authors describe an infant with both biliary atresia and hypoplastic left heart syndrome (HLHS) in the absence of a laterality defect or evidence of any other morphologic defect. The presence of a hypoplastic left ventricle in a patient with biliary atresia has previously been reported only in the context of a heterotaxy syndrome. The coexistence of these 2 disorders raises etiologic considerations and represents a potential challenge for the surgical treatment of both conditions.

Comments

This work was published before the author joined Aga Khan University.

Publication (Name of Journal)

Journal of Pediatric Surgery

Recommended Citation

Becker, D. J., Islam, S., Geiger, J. D. (2004). Biliary atresia associated with hypoplastic left heart syndrome: A case report and review of the literature. Journal of Pediatric Surgery, 39(9), 1411-1413.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_surg_paediatr/184