A rare case of constrictive pericarditis as initial manifestation of paediatric anaplastic large cell lymphoma requiring urgent pericardiectomy

Authors

Sara Iqbal, Aga Khan UniversityFollow
Abdul Ahad Sohail, Aga Khan UniversityFollow
Narmeen Asif, Aga Khan UniversityFollow
Muhammad Rahil Khan, Aga Khan University
Sabeehuddin Siddique, Aga Khan UniversityFollow
Saulat Fatimi, Aga Khan UniversityFollow

Document Type

Report

Department

Pathology and Laboratory Medicine; Cardiothoracic Surgery

Abstract

Constrictive pericarditis (CP) is a rare end stage inflammatory disorder affecting both parietal and visceral pericardium leading to a right heart failure. Malignancy is the least common cause of CP. Anaplastic large cell lymphoma (ALCL) accounts for 10-15% of all Non-Hodgkin lymphomas in children. Very few case reports have reported ALCL that is involving the heart and only two have been published involving pericardium but all were managed medically. We present an interesting case of an 11 year old child who presented with an effusive CP that required urgent Pericardiectomy for managing right heart failure. His histopathology was positive for ALK + ALCL.

Comments

Issue no. are not provided by the author/publisher

Publication (Name of Journal)

International Journal of Surgery Case Reports

Recommended Citation

Iqbal, S., Sohail, A. A., Asif, N., Khan, M. R., Siddique, S., Fatimi, S. (2020). A rare case of constrictive pericarditis as initial manifestation of paediatric anaplastic large cell lymphoma requiring urgent pericardiectomy. International Journal of Surgery Case Reports, 73, 281-284.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_surg_cardiothoracic/176

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