Hughes stovin syndrome: A case of recurrent pulmonary artery aneurysms

Authors

Mohammed Bin Pervez, Aga Khan University
Bilal Iqbal, Aga Khan UniversityFollow
Noreen Nasir, Aga Khan UniversityFollow
Saulat Fatimi, Aga Khan UniversityFollow

Document Type

Report

Department

Surgery; Cardiothoracic Surgery; Medicine; Internal Medicine

Abstract

HSS has around 40 cases recorded in literature. The disease process exhibits an indefinite nature. It shares histopathologic and clinical features with Behcets Disease, albeit there is no established association. The natural course of the disease is fatal in most cases. We report a case of a 31 year-old man with HSS, who initially presented with occasional hemoptysis and a history of deep vein thrombosis. There was evidence of right-sided lower lobe pulmonary artery aneurysm, which was managed with a lobectomy; post which he developed aneurysmal recurrence in the contralateral lung. Histopathology identified myxoid degeneration in the hilar region.

Comments

Volume, issue, and pagination are not provided by the author/publisher

Publication (Name of Journal)

Annals of Thoracic Surgery

Recommended Citation

Pervez, M. B., Iqbal, B., Nasir, N., Fatimi, S. (2020). Hughes stovin syndrome: A case of recurrent pulmonary artery aneurysms. Annals of Thoracic Surgery.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_surg_cardiothoracic/170