Hallervorden Spatz Disease is a rare familial neurodegenerative disorder, which primarily affects children but also can occur in adults1 . Major clinical features are abnormal involuntary movements and cognitive impairment2 . Diagnosis is based on clinical and radiological features. The radiological features are hypointense signals in globus pallidus and substantia niagra on MR! of brain3 . Occasionally the pallidal hypointense signals surround hyperintense signals, this is known as “tigereye-sign”4 and is postulated to be specific for Hallervorden Spatz Disease. We report two brothers with such MRI findings.
Journal of Pakistan Medical Association
Asumal, K. B.,
Ali, S. N.
(2002). Radiologic features of Hallervorden Spatz Disease. Journal of Pakistan Medical Association, 52(11), 528-530.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_med_neurol/168
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