Hallervorden Spatz Disease is a rare familial neurodegenerative disorder, which primarily affects children but also can occur in adults1 . Major clinical features are abnormal involuntary movements and cognitive impairment2 . Diagnosis is based on clinical and radiological features. The radiological features are hypointense signals in globus pallidus and substantia niagra on MR! of brain3 . Occasionally the pallidal hypointense signals surround hyperintense signals, this is known as “tigereye-sign”4 and is postulated to be specific for Hallervorden Spatz Disease. We report two brothers with such MRI findings.
Publication ( Name of Journal)
Journal of Pakistan Medical Association
Asumal, K. B.,
Ali, S. N.
(2002). Radiologic features of Hallervorden Spatz Disease. Journal of Pakistan Medical Association, 52(11), 528-530.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_med_neurol/168
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