Radiologic features of Hallervorden Spatz Disease

Authors

K B. Asumal, Aga Khan UniversityFollow
M Wasay, Aga Khan UniversityFollow
S N. Ali, Aga Khan UniversityFollow

Document Type

Report

Department

Neurology

Abstract

Hallervorden Spatz Disease is a rare familial neurodegenerative disorder, which primarily affects children but also can occur in adults1 . Major clinical features are abnormal involuntary movements and cognitive impairment2 . Diagnosis is based on clinical and radiological features. The radiological features are hypointense signals in globus pallidus and substantia niagra on MR! of brain3 . Occasionally the pallidal hypointense signals surround hyperintense signals, this is known as “tigereye-sign”4 and is postulated to be specific for Hallervorden Spatz Disease. We report two brothers with such MRI findings.

Publication (Name of Journal)

Journal of Pakistan Medical Association

Recommended Citation

Asumal, K. B., Wasay, M., Ali, S. N. (2002). Radiologic features of Hallervorden Spatz Disease. Journal of Pakistan Medical Association, 52(11), 528-530.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_med_neurol/168

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.