A rare aetiology of respiratory failure in a 10-year-old boy: inflammatory myofibroblastic tumour.

Authors

Ali Khawaja, Aga Khan University
Prem Kumar Maheshwar, Aga Khan University
Anwarul Haque, Agha Khan UniversityFollow
Ali Bin Sarwar Zubairi, Department of Pulmonary and Critical Care Medicine, The Aga Khan UniversityFollow

Document Type

Report

Department

Medicine

Abstract

Primary neoplasms of the respiratory tract are rarely encountered in the paediatric population. Inflammatory myofibroblastic tumour (IMT) is a rare soft tissue mesenchymal tumour but a distinct disease entity accounting for less than 1% of all primary lung tumours. We report a case of a 10-year-old boy who presented with respiratory failure and left lung collapse. On flexible fiberoptic bronchoscopy, a pedunculated mass in the lower part of the trachea originating from the left main stem bronchus was identified. The patient subsequently underwent a left-sided pneumonectomy with complete resection of the mass. The histopathological analysis was consistent with IMT. Two years of follow-up and the patient remains well.

Comments

CASE REPORT.

NOTE: VOL & ISSUE #, PAGES : NOT FOUND.

Publication (Name of Journal)

BMJ case reports.

Recommended Citation

Khawaja, A., Maheshwar, P. K., Haque, A., Zubairi, A. (2013). A rare aetiology of respiratory failure in a 10-year-old boy: inflammatory myofibroblastic tumour.. BMJ case reports..
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_med_med/294