Complicated unroofed coronary sinus syndrome

Ghulam Sarwar, Aga Khan University
Bilal Ahmed, Aga Khan University
Naeem Suleman
Ghufranullah Khan


A young boy planned for the surgical closure of atrial septal defect (ASD) and mitral valve regurgitation (MR) was found peroperatively as having a complete unroofed coronary sinus (URCS). Intracardiac re-routing of left superior vena cava (LSVC) and mitral valve replacement (MVR) were performed concomitantly with success.