Document Type

Case Report

Department

Internal Medicine (East Africa)

Abstract

Pseudomyxoma peritonei (PMP) is a rare condition resulting from mucin-producing tumors that have disseminated intointraperitoneal implants and mucinous ascites. The extra-abdominal spread of PMP is exceptionally rare, with few reportedcases in the medical literature. Pseudomyxoma pleurii is an infrequently encountered clinical syndrome characterized bytransdiaphragmatic pleural extension and spread of PMP. The disease is highly fatal. We hereby report a case of 58 years oldwoman who presented with an abdominal distension and shortness of breath of 2 months duration. Histopathology confirmedthe diagnosis of large mucin-producing rectosigmoid adenomatous polypoid lesion with malignant transformation and PMPthat had spread to the right pleural space. PMP from colon tumor is uncommon and its transdiaphragmatic pleural extensionis very unusual complicated by management challenge and high mortality rate.

Comments

This work was published before the author joined Aga Khan University.

Publication (Name of Journal)

Oxford Medical Case Reports

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