Internal Medicine (East Africa)
Caroli disease and Caroli syndrome are two rare congenital diseases of the intrahepatic bileducts. Caroli syndrome is characterized by the saccular dilatation of intrahepatic bile ductsassociated with congenital hepatic fibrosis. It is rarely diagnosed in childhood. We herebydescribe a case of Caroli syndrome in a young Tanzanian female who had abdominal pain anddistension since childhood. Her history suggested the presence of portal hypertension possiblyfrom congenital hepatic fibrosis. The diagnosis was reached based on ultrasound, computedtomography (CT) scan of the abdomen, and magnetic resonancecholangiopancreatography (MRCP)
Casmir, W., Sharma, M., & Salim, S. (2020). Revisiting Caroli Syndrome in a Tanzanian Patient. Cureus, 12(1).
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