Revisiting Caroli Syndrome in a Tanzanian Patient

Authors

Casmir Wambura, Aga Khan UniversityFollow
Munish Sharma, Corpus Christi Medical Center
Salim Surani, Texas A&M Health Science Center

Document Type

Case Report

Department

Internal Medicine (East Africa)

Abstract

Caroli disease and Caroli syndrome are two rare congenital diseases of the intrahepatic bile ducts. Caroli syndrome is characterized by the saccular dilatation of intrahepatic bile ducts associated with congenital hepatic fibrosis. It is rarely diagnosed in childhood. We hereby describe a case of Caroli syndrome in a young Tanzanian female who had abdominal pain and distension since childhood. Her history suggested the presence of portal hypertension possibly from congenital hepatic fibrosis. The diagnosis was reached based on ultrasound, computed tomography (CT) scan of the abdomen, and magnetic resonance cholangiopancreatography (MRCP).

Comments

This work was published after the author joined Aga Khan University.

Publication (Name of Journal)

Cureus

Recommended Citation

Wambura, C., Sharma, M., & Surani, S. (2020). Revisiting Caroli syndrome in a Tanzanian patient. Cureus, 12(1).