Paediatrics and Child Health
Idiopathic pulmonary haemosiderosis is an uncommon disorder, which is characterized by iron deficiency, recurrent haemoptysis and diffuse parenchymal infiltration on chest radiograph. We report an 8 year old child who had past history of multiple blood transfusions with diagnosis of iron deficiency anaemia and recurrent chest infection since the age of 21/2 year. At the age of 8 years, the child presented with fever and severe respiratory distress requiring intubation and ventilation. On Chest X-ray, bilateral white out was found and CT scan lung showed diffuse alveolar involvement. Lung biopsy confirmed haemosiderin-laden macrophages. Child was put on steroids and despite severe anaemia (Hb 3.2 g/dl), he showed improvement and survived. To our knowledge, this is the first case of idiopathic pulmonary haemosiderosis reported from Pakistan.
Journal of Pakistan Medical Association
(2012). Idiopathic pulmonary haemosiderosis presenting as severe iron deficiency anaemia--a case from Pakistan. Journal of Pakistan Medical Association, 62(8), 845-847.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_women_childhealth_paediatr/513