Moyamoya disease presenting with intracranial haemorrhàge

Ali Akbar, Department of Neurosurgery, Jinnah Postgraduate Medical Centre, Karachi.
Aftab Qureshi, Department of Neurosurgery, Jinnah Postgraduate Medical Centre, Karachi
Rashid Jooma, Aga Khan University

This work was published before the author (Rashid Jooma) joined Aga Khan University.


Moyamoya disease is a spontaneous occlusion of the circle of Willis withabnonnalcompensatoryanastamoticvascular networks at the base of the brain. Early reportscharacterisedthe condition as a cause of cerebralischaemiawith progressive neurological deficits in infants and children or intracranialhaemorrhagein adolescents and adults of Japanese Community1,2. However, it is now well known to occur in the other parts of the world as well - though being contingent onangiographicfindings, the diagnosisdependon the level of the nation’s health care provision. Two cases ofmoyamoyadiseases admitted toneurosurgical unitwith intracranialhaemorrhageare being presented here.