Hughes stovin syndrome: A case of recurrent pulmonary artery aneurysms
Surgery; Cardiothoracic Surgery; Medicine; Internal Medicine
HSS has around 40 cases recorded in literature. The disease process exhibits an indefinite nature. It shares histopathologic and clinical features with Behcets Disease, albeit there is no established association. The natural course of the disease is fatal in most cases. We report a case of a 31 year-old man with HSS, who initially presented with occasional hemoptysis and a history of deep vein thrombosis. There was evidence of right-sided lower lobe pulmonary artery aneurysm, which was managed with a lobectomy; post which he developed aneurysmal recurrence in the contralateral lung. Histopathology identified myxoid degeneration in the hilar region.
Annals of Thoracic Surgery
Pervez, M. B.,
(2020). Hughes stovin syndrome: A case of recurrent pulmonary artery aneurysms. Annals of Thoracic Surgery.
Available at: https://ecommons.aku.edu/pakistan_fhs_mc_surg_cardiothoracic/170