Re-recurrent Dermatofibrosarcomaprotuberans of the chest wall

Niaz Hussain, Ojha Institute of Chest Disease and Dow University Hospital
Mujtaba Zaki i Naveed,, Aga Khan University
Ghulam H, Aga Khan University

case Reports.


Dermatofibrosarcomaprotuberans is a rare, soft tissue tumour with high rate of recurrence. It is locally aggressive, with a low rate of metastasis. We describe the case of a 42 year old man who presented with a rerecurrent, large tumoursituated on the anterior chest wall in the sternal region. We did a wide local excision and covered the resulting defect by using bilateral, pectoralis major myocutaneous flaps. Histopathology and immunohistochemical staining findings were consistent with the diagnosis of Dermatofibrosarcoma Protuberance. Post operatively the patient was treated with chemotherapy and radiotherapy