Acute myelofibrosis and multiple chloromas of the mandible and skin

Document Type

Article

Department

Haematology and Oncology, East Africa

Abstract

Acute myelofibrosis is a rare clinical entity characterized by severe marrow fibrosis and peripheral blood pancytopenia. It may be very closely related to and has been considered synonymous with megakaryocytic leukemia. Chloroma is also a rare entity composed of a localized collection of immature myeloid cells and is associated with a known or covert leukemia. A patient presenting with a rare combination of acute myelofibrosis, megakaryocytic leukemia and multiple chloromas of the mandible and skin, are described. Although presenting a diagnostic challenge, their combination in one patient aids in the understanding of the myeloproliferative process. To our knowledge, this is the 3rd case of chloroma involving the oral osseous structures.

Comments

This work was published before the author joined Aga Khan University.

Publication (Name of Journal)

International journal of oral and maxillofacial surgery

DOI

https://doi.org/10.1016/S0901-5027(87)80039-5

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