Congenital pyloric atresia with epidermolysis bullosa is recognized as a rare but distinct entity which is uniformly fatal1,2. Until 1990 only 20 cases have been reported in the English literature3,4. We present an additional case managed at the Aga Khan University Hospital to demonstrate the difficulties encountered in the management of such infants.
Journal of the Pakistan Medical Association
(1991). Congenital pyloric atresia and epidermolysis bullosa. Journal of the Pakistan Medical Association, 41(10), 254-256.
Available at: http://ecommons.aku.edu/pakistan_fhs_mc_surg_paediatr/22