In 1898 Banti described a disorder characterized by splenomegaly and hypersplenism, resulting in portal hypertension and anemia in the absence of hematological disease. 1 Banti's syndrome is also known as non-cirrhotic portal hypertension (NCPH) in India and Idiopathic Portal Hypertension (IPH) in Japan. Hepatoportal sclerosis seems to be its counterpart in the United States. 2,3 Banti's syndrome is a disorder of unknown etiology, clinically characterized by portal hypertension (varices and portosystemic collateral vessels), splenomegaly, and anemia (hypersplenism). 3 It has been reported from Indian subcontinent. 4-6 In a Pakistani case series of portal hypertension, 18 out of 37 patients were found to have IPH as the etiology. 6 We report a case of Banti's syndrome in an 20-year old girl presenting to us with anemia and splenomegaly.
Journal of Pakistan Medical Association
(2004). Banti's syndrome: case report and review of literature. Journal of Pakistan Medical Association, 54(2), 99-101.
Available at: http://ecommons.aku.edu/pakistan_fhs_mc_med_intern_med/28