Epidermolysis bullosa is a group of inherited disorders characterized by blistering of the skin as a result of minor trauma. We managed an infant with epidermolysis bullosa undergoing inguinal hernia repair. Anaesthesia was induced with oxygen/nitrous oxide mixture and sevoflurane. Oral tracheal intubation was done with a lubricated laryngoscope blade with KY jelly using atracurium 0.5 mg/kg and fentanyl 0.1 microgm/kg. To avoid frictions on the skin, endotracheal tube was tied with ribbon gauze and fixed around the neck. Pulse-oximetry probe and electrocardiogram electrodes were placed, and then attached to the patient's skin covered with KY jelly. Peripheral venous access was secured in the right foot and sutured. These methods were effective to avoid new blisters and useful for infant safety.
Journal of the Pakistan Medical Association
(2010). Anaesthetic management of an infant with epidermolysis bullosa undergoing inguinal hernia repair. Journal of the Pakistan Medical Association, 60(6), 497-8.
Available at: http://ecommons.aku.edu/pakistan_fhs_mc_anaesth/23